Hyperimmunoglobulin E syndrome
AUTOSOMAL DOMINANT FORM CALLED JOB'S SYNDROME OR BUCKLEY SYNDROME, IS A HETEROGENEOUS GROUP OF IMMUNE DISORDERS
Hyper IgE Syndrome; Job syndrome; Job's syndrome; Hyper IgE syndrome; Job-Buckley syndrome; Buckley syndrome; Hyper-immunoglobulin E syndrome; Hyper IgE; Hyperimmunoglobulinemia E; Hyperimmunoglobulinemia E syndrome; Hyper-IgE syndrome; Buckley's syndrome; Hyper-IgE; Retention of primary teeth
Hyperimmunoglobulinemia E syndrome (HIES), of which the autosomal dominant form is called Job's syndrome or Buckley syndrome, is a heterogeneous group of immune disorders. Job's is also very rare at about 300 cases currently in the literature.